Sunday, July 1, 2012

Understanding Rett Syndrome

Rett Syndrome is a Pervasive Developmental Disorder discovered by Dr. Andreas Rett, an Austrian pediatrician who in the late 1950's noticed that a few of his patients shared similar characteristics such as hand-wringling. Dr. Rett soon disovered similar cases in other parts of Euope. After publish a paper on the cases in a professional journal, other cases were noted in the United States.
Epidemiology

Rett Syndrome is rare and will affect 1/10,000 females
75% will lose their ability to walk in later years.
85% will develop scoliosis
Caused by a mutation in the gene which is believed to control the functions of many genes.

Symptoms

The child may appear normal for the first 6-18 months
will begin to lose:
  • loss of finger skills
  • loss of communication skills
  • deceleration of head growth
  • will develop scoliosis
Many believe that Rett Syndrome should not be placed in the catergory of PDD since it is a neurological disorder because of distinct differences such as in some cases, eye contct is maintained and hand movements are very different from the motor stereotypes of a person with autism.

Understanding Rett Syndrome


No comments: